Aim: To present a rare case of extranasopharyngeal angiofibroma (ENA) in a female originating from uncinate process in nasal cavity. Background: Nasopharyngeal angiofibroma is a rare vascular tumor affecting adolescent male. It is the most common benign tumor of nasopharynx. Angiofibroma located outside the nasopharyngeal area are extremely rare and, consequently, may be misdiagnosed. Unlike nasopharyngeal angiofibroma, symptoms of ENAs are nonspecific and depend on localization and extent of tumor. The occurrence of any nasopharyngeal angiofibroma in females is very rare. Also, ENA has been reported at various subsites in nasal cavity, but origin from uncinate process is not reported in world literature till date. So we are reporting this unique case. Case description: A 40-year-old female presented with intermittent profuse bleeding diagnosed as ENA originating from uncinate process. Tumor is removed completely through lateral rhinotomy approach. Conclusion: Extranasopharyngeal angiofibroma is a rare tumor but it should be kept in differential diagnosis of vascular tumor of nose and paranasal area. Surgical excision is the treatment of choice for angiofibroma of nose and paranasal sinuses. Clinical significance: Extranasopharyngeal angiofibromas can originate from various subsites of nasal cavity including uncinate process. Patients affected are older, symptoms develop more quickly, and hypervascularity is less common.