Clinical Rhinology

Register      Login

SEARCH WITHIN CONTENT

FIND ARTICLE

Volume / Issue

Online First

Archive
Volume  14 (2023)
Volume  13 (2020)
Volume  12 (2019)
Volume  11 (2018)
Volume  10 (2017)
Volume  9 (2016)
Volume  8 (2015)
Volume  7 (2014)
Volume  6 (2013)
Volume  5 (2012)
Volume  4 (2011)
Volume  3 (2010)
Volume  2 (2009)
Related articles

VOLUME 9 , ISSUE 1 ( January-April, 2016 ) > List of Articles

CASE REPORT

Ectodermal Dysplasia presenting with Atrophic Rhinitis: A Report of Two Cases and a Review of the Literature

Sampurna Pati, Sudipta Pal, Surajit Biswas, Somnath Saha

Keywords : Atrophic rhinitis,Ectodermal dysplasia,Nasal myiasis

Citation Information : Pati S, Pal S, Biswas S, Saha S. Ectodermal Dysplasia presenting with Atrophic Rhinitis: A Report of Two Cases and a Review of the Literature. Clin Rhinol An Int J 2016; 9 (1):53-55.

DOI: 10.5005/jp-journals-10013-1266

Published Online: 01-04-2016

Copyright Statement:  Copyright © 2016; The Author(s).


Abstract

Aims

To present two rare cases of ectodermal dysplasia presenting with maggot infestation due to atrophic rhinitis.

Study design

Case report.

Setting

A tertiary care referral hospital.

Presentation

Two male children aged about 5 and 8 years presented to the ear, nose, and throat emergency with a history of maggot infestation of the nose.

Results

Clinical examination was suggestive of ectodermal dysplasia. Intranasal examination was suggestive of atrophic rhinitis. Maggots were removed in the conventional manner. Following a conservative treatment, skin biopsy and nasal mucosal biopsy were done, which confirmed the diagnosis of ectodermal dysplasia.

Conclusion

Any ectodermal dysplasia patient should be suspected of having atrophic rhinitis and intranasal conservative therapy should be initiated at the earliest to prevent complications like maggots in the nose.

How to cite this article

Pati S, Pal S, Saha S, Biswas S. Ectodermal Dysplasia presenting with Atrophic Rhinitis: A Report of Two Cases and a Review of the Literature. Clin Rhinol An Int J 2016;9(1):53-55.

PDF Share
  1. Two cases in which the skin, hair and teeth were very imperfectly developed. Med Chir Trans 1848;31: 71-82.
  2. Hereditary ectodermal dysplasia (congenital ectodermal defect). Am J Dis Child 1929;37:766-790.
  3. On the distribution of frequencies of mutation to genes determining harmful traits in man. Mutat Res 1967 May;4(3):339-352.
  4. Ocular symptoms and signs in patients with ectodermal dysplasia syndromes. Graefes Arch Clin Exp Ophthalmol 2004 Jun;242(6):495-500.
  5. Salivary gland function in persons with ectodermal dysplasias. Eur J Oral Sci 2003 Oct;111(5):371-376.
  6. Ectodermal dysplasia: Otolaryngologic manifestations and management. Laryngoscope 2002 Jun;112(6):962-967.
  7. Rhinologic manifestations of ectodermal dysplasia. Am J Rhinol 2007 Jan-Feb;21(1):55-58.
  8. Growth characteristics of children with ectodermal dysplasia syndromes. Pediatrics 2005 Aug;116(2):e229-e234.
  9. Anhidrotic ectodermal dysplasia presenting as atrophic rhinitis. J Laryngol Otol 2004 Jul;118(7):556-557.
  10. Atrophic rhinitis in a patient w anhidrotic ectodermal dysplasia. Rhinology 2005 Sep;43(3):233-235.
  11. Hypohydrotic (Anhydrotic) Ectodermal dysplasia -A rare cause of childhood atrophic rhinitis. Indian J Otolaryngol Head Neck Surg 2006 Apr;58(2):202-204.
  12. Hypohidrotic ectodermal dysplasia with atrophic rhinitis and nasal myiasis. Int J Pediatr Otorhinolaryngol 2009 Oct;73(10):1467-1469.
  13. Anhidrotic ectodermal dysplasia presenting as atrophic rhinitis. J Indian Med Assoc 2011 Nov;109(11):836-837.
  14. ; Hansen, RC., editors. Pediatric dermatology: Ectodermal dysplasia. 2nd ed. Vol. I. New York: Churchill Livingstone; 1995. p. 361-363.
PDF Share
PDF Share

© Jaypee Brothers Medical Publishers (P) LTD.