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VOLUME 8 , ISSUE 3 ( September-December, 2015 ) > List of Articles

CASE REPORT

Ectodermal Dysplasia Presenting with Atrophic Rhinitis: Report of Two Cases and Review of Literature

Sampurna Pati, Sudipta Pal, Somnath Saha, Surajit Biswas

Keywords : Atrophic rhinitis,Ectodermal dysplasia,Nasal myiasis

Citation Information : Pati S, Pal S, Saha S, Biswas S. Ectodermal Dysplasia Presenting with Atrophic Rhinitis: Report of Two Cases and Review of Literature. Clin Rhinol An Int J 2015; 8 (3):133-135.

DOI: 10.5005/jp-journals-10013-1252

Published Online: 01-12-2015

Copyright Statement:  Copyright © 2015; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Aim

To present two rare case of ectodermal dysplasia presenting with maggot infestation due to atrophic rhinitis.

Study design

Case report.

Setting

Tertiary care referral hospital.

Presentation

Two male child aged about 5 and 8 years presented in ENT emergency with history of maggot infestation of nose.

Result

Clinical examination was suggestive of ectodermal dysplasia. Intranasal examination was suggestive of atrophic rhinitis. Maggots were removed in conventional manner. Following conservative treatment, skin biopsy and nasal mucosal biopsy was taken which confirmed the diagnosis of ectodermal dysplasia.

Conclusion

Any ectodermal dysplasia patient should be suspected of having atrophic rhinitis and intranasal conservative therapy should be initiated at the earliest to prevent complication like maggots in nose.

How to cite this article

Pati S, Pal S, Saha S, Biswas S. Ectodermal Dysplasia Presenting with Atrophic Rhinitis: Report of Two Cases and Review of Literature. Clin Rhinol An Int J 2015;8(3):133-135.

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  1. Two cases in which the skin, hair and teeth were very imperfectly developed. Proc RM Chir Soc 1848;31:71-82.
  2. Hereditary ectodermal dysplasia (congenital ectodermal defect). Am J Dis Child 1929;37:766-790.
  3. Mulat Res 1967;4:339-352.
  4. Ocular symptoms and signs in patients with ectodermal dysplasia syndromes. Graefes Arch Clin Exp Ophthalmol 2004 Jun;242(6):495-500.
  5. Salivary gland function in persons with ectodermal dysplasias. Eur J Oral Sci 2003 Oct;111(5):371-376.
  6. Ectodermal dysplasia: otolaryngologic manifestations and management. Laryngoscope 2002 Jun;112(6):962-967.
  7. Rhinologic manifestations of ectodermal dysplasia. Am J Rhinol 2007 Jan-Feb;21(1):55-58.
  8. Growth characteristics of children with ectodermal dysplasia syndromes. Pediatrics 2005 Aug;116(2):e229-234.
  9. Anhidrotic ectodermal dysplasia presenting as atrophic rhinitis. J Laryngol Otol 2004 Jul;118(7):556-557.
  10. Atrophic rhinitis in a patient w anhidrotic ectodermal dysplasia. Rhinology 2005 Sep;43(3):233-235.
  11. Hypohydrotic (anhydrotic ectodermal dysplasia-a rare cause of childhood atrophic rhinitis. Ind J Otolaryngol Head Neck Surg 2006 Apr;58(2):202-204.
  12. Hy pohidrotic ectodermal dysplasia with atrophic rhinitis and nasal myiasis. Int J Pediatr Otorhinolaryngol 2009;73:1467-1469.
  13. Anhidrotic ectodermal dysplasia presenting as atrophic rhinitis. J Ind Med Assoc 2011 Nov;109(11):836-837.
  14. Edited by Laurence A, Schachner and Ronald C. Hansen. 2nd ed. Churchill Livingstone, New York, 1995. p. 361-363.
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