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VOLUME 8 , ISSUE 3 ( September-December, 2015 ) > List of Articles

CASE REPORT

Ectodermal Dysplasia Presenting with Atrophic Rhinitis: Report of Two Cases and Review of Literature

Sampurna Pati, Sudipta Pal, Somnath Saha, Surajit Biswas

Keywords : Atrophic rhinitis,Ectodermal dysplasia,Nasal myiasis

Citation Information : Pati S, Pal S, Saha S, Biswas S. Ectodermal Dysplasia Presenting with Atrophic Rhinitis: Report of Two Cases and Review of Literature. Clin Rhinol An Int J 2015; 8 (3):133-135.

DOI: 10.5005/jp-journals-10013-1252

Published Online: 00-12-2015

Copyright Statement:  Copyright © 2015; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Aim

To present two rare case of ectodermal dysplasia presenting with maggot infestation due to atrophic rhinitis.

Study design

Case report.

Setting

Tertiary care referral hospital.

Presentation

Two male child aged about 5 and 8 years presented in ENT emergency with history of maggot infestation of nose.

Result

Clinical examination was suggestive of ectodermal dysplasia. Intranasal examination was suggestive of atrophic rhinitis. Maggots were removed in conventional manner. Following conservative treatment, skin biopsy and nasal mucosal biopsy was taken which confirmed the diagnosis of ectodermal dysplasia.

Conclusion

Any ectodermal dysplasia patient should be suspected of having atrophic rhinitis and intranasal conservative therapy should be initiated at the earliest to prevent complication like maggots in nose.

How to cite this article

Pati S, Pal S, Saha S, Biswas S. Ectodermal Dysplasia Presenting with Atrophic Rhinitis: Report of Two Cases and Review of Literature. Clin Rhinol An Int J 2015;8(3):133-135.


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