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VOLUME 7 , ISSUE 1 ( January-April, 2014 ) > List of Articles

CASE REPORT

Our Experiences with Congenital Midline Nasal Dermoid Sinus Cyst

Yashwant Maru, Yamini Gupta

Keywords : Congenital nasal sinus,Development,Nasal midline sinus

Citation Information : Maru Y, Gupta Y. Our Experiences with Congenital Midline Nasal Dermoid Sinus Cyst. Clin Rhinol An Int J 2014; 7 (1):43-46.

DOI: 10.5005/jp-journals-10013-1192

Published Online: 00-04-2014

Copyright Statement:  Copyright © 2014; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Introduction

Nasofrontal dermoid sinus cysts (NDSC) are rare congenital malformations. NDSCs are distinct from other facial dermoids in their potential for involving deeper contiguous structures and intracranial extension. The development of this congenital midline sinus of dorsum of nose has opened a new horizon in current concepts of embryology.

Objective

To study the embryological origin, presentation, treatment, and genetic associations of three cases of these sinus cysts.

Clinical presentation

This paper presents our experiences with managing three patients who presented with opening on nasal dorsum with recurrent swelling and purulent discharge from it. Imaging studies in these patients indicated a midline anterior nasal sinus tract with cranial dilatation but no intracranial connection. They were successfully managed surgically.

Conclusion

Nasofrontal dermoid sinus cysts have a unique embryological origin. A midline basal frontal dermoid associated with a dimple or sinus opening on the nasal dorsum with or without protruding hair and sebaceous discharge is the classical presentation. The purpose of this report is to emphasize that, though rare nasofrontal dermoid sinus cysts do occur in our practice and their clinical importance from rhinology point of view is their potential for intracranial communication.

How to cite this article

Maru Y, Gupta Y. Our Experiences with Congenital Midline Nasal Dermoid Sinus Cyst. Clin Rhinol An Int J 2014;7(1):43-46.


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