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VOLUME 13 , ISSUE 1 ( January-April, 2020 ) > List of Articles

CASE REPORT

Endoscopic Endonasal Management of Extraskeletal Sinonasal Ewing's Sarcoma

Anuragini Gupta, Sushmita Gupta, Deepika Chaudhary, Anish Gupta, Ashok K Gupta

Keywords : Endoscopic, Endoscopic excision, Rare

Citation Information : Gupta A, Gupta S, Chaudhary D, Gupta A, Gupta AK. Endoscopic Endonasal Management of Extraskeletal Sinonasal Ewing's Sarcoma. Clin Rhinol An Int J 2020; 13 (1):15-17.

DOI: 10.5005/jp-journals-10013-1370

License: CC BY-NC 4.0

Published Online: 00-04-2020

Copyright Statement:  Copyright © 2020; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Ewing\'s sarcoma (ES) is a primary neoplasm of the skeletal system. Ewing\'s sarcoma of the head-and-neck region constitutes about 1–4% of extraskeletal Ewing\'s sarcoma (EES cases). Sinonasal EES is extremely rare and there is limited literature on this entity. Establishing the diagnosis requires a histopathological examination, immunohistochemistry, and a cytogenetic analysis along with a CT scan and MRI of the paranasal sinuses. They require multimodality treatment including surgical resection followed by chemotherapy and/or radiotherapy. We present a case report of a 31-year-old male patient presenting with a right-sided headache associated with nausea and vomiting, right nasal obstruction, a mass protruding from the right nostril and associated with occasional nasal bleed for 4 months with aggravation of symptoms since last 15 days along with proptosis of the right eye. On nasal examination, reddish-brown friable slough covered mass protruding from the right nostril bleeding on manipulation. Endoscopic endonasal excision biopsy revealed a round cell tumor-ES/primitive neuroectodermal tumor (PNET). The patient received radiotherapy and chemotherapy postoperatively and is on regular follow-up for 2 years and is disease-free.


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